Familial nesidioblastosis
نویسندگان
چکیده
منابع مشابه
Hyperinsulinaemic hypoglycaemia due to chlorpropamide-induced nesidioblastosis.
A 25 year old woman suffering from recurrent attacks of hypoglycaemia underwent a laparotomy for suspected insulinoma. No tumour was found, but histology showed islet cell hyperplasia and nesidioblastosis. Although these changes have been reported as a cause of hypoglycaemia in infants, they are only rarely the cause of hypoglycaemia in adults; in the present case they were found to be the resu...
متن کاملNesidioblastosis in the Adult Surgical Management
Nesidioblastosis is an exceedingly rare occurrence in the adult and, when it appears, it is usually part of a MEA1 syndrome. We present a case of nesidioblastosis in a young woman, with no concurrent endocrine pathology, while we discuss in detail the diagnostic and therapeutic problems posed by this condition. The selected treatment was sub-total pancreatectomy (70-80%) and the histopathologic...
متن کاملAdult onset nesidioblastosis treated by subtotal pancreatectomy.
CONTEXT Nesidioblastosis is a rare cause of non insulinoma pancreatogenous hypoglycemic syndrome seen in adults. It is characterized by postprandial hypoglycemia with high insulin and C-peptide levels without any detectable pancreatic lesion. The definitive diagnosis can be made only on histopathological examination of the resected specimen. CASE REPORT We report a case of a 50-year-old lady ...
متن کاملDiffuse nesidioblastosis with hypoglycemia mimicking an insulinoma: a case report
INTRODUCTION We describe a case of diffuse nesidioblastosis in an adult patient who presented with exclusively fasting symptoms and a focal pancreatic 111In-pentetreotide uptake mimicking an insulinoma. CASE PRESENTATION A 23-year-old Caucasian man had severe daily fasting hypoglycemia with glucose levels below 2mmol/L. Besides rare neuroglycopenic symptoms (confusion, sleepiness), he was lar...
متن کاملHypopituitarism and nesidioblastosis in an elderly patient with orbital lymphoma.
Nesidioblastosis is a rare cause of hyperinsulinemic hypoglycemia in adults. We report a case of combined hypopituitarism with secondary adrenal insufficiency and nesidioblastosis with symptomatic hypoglycemia. This 84-year-old woman had a diagnosis of right side orbital lymphoma and underwent one complete course of local radiotherapy 6 months prior to this admission. Intermittent consciousness...
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ژورنال
عنوان ژورنال: Pediatric Research
سال: 1979
ISSN: 0031-3998,1530-0447
DOI: 10.1203/00006450-197901000-00097